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References from Extracellular matrix abnormalities in Hutchinson–Gilford progeria fibroblasts: a specific defect in collagen IV and basement membrane architecture?. Local targets link to admitted publications; unresolved targets remain external evidence.
Phenotype and course of Hutchinson-Gilford progeria syndrome
10.1056/nejmoa0706898 · 2008 · External reference
Recurrent de novo point mutations in lamin A cause Hutchinson–Gilford progeria syndrome
10.1038/nature01629 · 2003 · External reference
Accumulation of mutant Lamin a causes progressive changes in nuclear architecture in Hutchinson-Gilford progeria syndrome
10.1073/pnas.0402943101 · 2004 · External reference
Progeria kidney has abnormal mesangial collagen distribution
10.1007/s004670000479 · 2000 · External reference
Smooth muscle cell depletion and collagen types in progeric arteries
10.1016/s1054-8807(01)00069-2 · 2001 · External reference
Cardiovascular pathology in Hutchinson-Gilford progeria: correlation with the vascular pathology of aging
10.1161/atvbaha.110.209460 · 2010 · External reference
Severe bone changes in a case of Hutchinson-Gilford syndrome
10.1016/s0003-3995(02)01119-x · 2002 · External reference
Progeria (Hutchinson-Gilford)
10.1001/archderm.1973.01620170061016 · 1973 · External reference
Inflammation and fibrosis in progeria: organ-specific responses in an HGPS mouse model
10.3390/ijms25179323 · 2024 · External reference
Hutchinson-Gilford progeria syndrome
10.1001/jamadermatol.2025.0793 · 2025 · External reference
Endothelial YAP/TAZ activation promotes atherosclerosis in a mouse model of Hutchinson-Gilford progeria syndrome
10.1172/jci173448 · 2024 · External reference
Functional coupling between the extracellular matrix and nuclear lamina by Wnt signaling in progeria
10.1016/j.devcel.2010.08.013 · 2010 · External reference
Transcriptional profiling of Hutchinson-Gilford progeria syndrome fibroblasts reveals deficits in mesenchymal stem cell commitment to differentiation related to early events in endochondral ossification
10.7554/elife.81290 · 2022 · External reference
Critical re-examination of the premature aging concept in progeria: a light and electron microscopic study
10.1016/0047-6374(73)90018-3 · 1973 · External reference
PRELP, collagen, and a theory of Hutchinson-Gilford progeria
10.1016/s1568-1637(02)00044-2 · 2003 · External reference
Epigenetic deregulation of lamina-associated domains in Hutchinson-Gilford progeria syndrome
10.1186/s13073-020-00749-y · 2020 · External reference
Phosphorylated Lamin a/C in the nuclear interior binds active enhancers associated with abnormal transcription in progeria
10.1016/j.devcel.2020.02.011 · 2020 · External reference
A cell-intrinsic interferon-like response links replication stress to cellular aging caused by Progerin
10.1016/j.celrep.2018.01.090 · 2018 · External reference
Genome-scale expression profiling of Hutchinson-Gilford progeria syndrome reveals widespread transcriptional misregulation leading to mesodermal/mesenchymal defects and accelerated atherosclerosis
10.1111/j.1474-9728.2004.00105.x · 2004 · External reference
Aging of Hutchinson-Gilford progeria syndrome fibroblasts is characterised by hyperproliferation and increased apoptosis
10.1016/j.exger.2004.02.002 · 2004 · External reference
A perinuclear actin cap regulates nuclear shape
10.1073/pnas.0908686106 · 2009 · External reference
Dysfunctional connections between the nucleus and the actin and microtubule networks in laminopathic models
10.1529/biophysj.108.139428 · 2008 · External reference
Long-term imaging of cellular forces with high precision by elastic resonator interference stress microscopy
10.1038/ncb3561 · 2017 · External reference
Highly transparent elastic optical microcavities for interferometric mapping of cell mechanics
10.1364/boe.572738 · 2025 · External reference
Dynamics of basement membrane formation by keratinocyte-fibroblast interactions in organotypic skin culture
10.1006/excr.1997.3910 · 1998 · External reference
Basement membrane reconstruction in human skin equivalents is regulated by fibroblasts and/or exogenously activated keratinocytes
10.1111/j.0022-202x.2004.23549.x · 2005 · External reference
Transcriptional profiling of Hutchinson-Gilford progeria patients identifies primary target pathways of progerin
10.1080/19491034.2025.2611484 · 2026 · External reference
Notch signaling pathway induces expression of type IV collagen in angiogenesis
10.1093/jb/mvad120 · 2024 · External reference
Regulation of extracellular matrix synthesis by mechanical stress
10.1139/o96-080 · 1996 · External reference
Progerin accelerates atherosclerosis by inducing endoplasmic reticulum stress in vascular smooth muscle cells
10.15252/emmm.201809736 · 2019 · External reference
Age-related changes in normal human basement membrane
10.1016/0047-6374(82)90015-x · 1982 · External reference
Changes of the basement membrane and type IV collagen in human skin during aging
10.1016/s0378-5122(96)01066-3 · 1996 · External reference
Aging decreases collagen IV expression in vivo in the dermo-epidermal junction and in vitro in dermal fibroblasts: possible involvement of TGF-β1
10.1684/ejd.2016.2782 · 2016 · External reference
Fibroblasts in mechanically stressed collagen lattices assume a “synthetic” phenotype
10.1074/jbc.m101602200 · 2001 · External reference
10.1155/2023/6892763
10.1155/2023/6892763 · External reference
Recombinant nidogen consists of three globular domains and mediates binding of laminin to collagen type IV
10.1002/j.1460-2075.1991.tb04875.x · 1991 · External reference
Cell-populated collagen lattice models
10.1007/978-1-4939-7113-8_15 · 2017 · External reference
Living tissue formed in vitro and accepted as skin-equivalent tissue of full thickness
10.1126/science.7008197 · 1981 · External reference
