Research graph
References from Ganglioside profiling by ion mobility and mass spectrometry imaging identifies distinct biomolecular isomers in Niemann-Pick Disease. Local targets link to admitted publications; unresolved targets remain external evidence.
Endothelial and neuronal engagement by AAV-BR1 gene therapy alleviates neurological symptoms and lipid deposition in a mouse model of Niemann-Pick type C2
10.1186/s12987-025-00621-4 · 2025 · External reference
Neurons in Niemann-Pick Disease Type C Accumulate Gangliosides as Well as Unesterified Cholesterol and Undergo Dendritic and Axonal Alterations
10.1093/jnen/60.1.49 · 2001 · External reference
10.1194/jlr.d086090
10.1194/jlr.d086090 · External reference
10.1016/j.febslet.2010.04.047
10.1016/j.febslet.2010.04.047 · External reference
Neurodegeneration in Niemann–Pick Type C Disease: An Updated Review on Pharmacological and Non-Pharmacological Approaches to Counteract Brain and Cognitive Impairment
10.3390/ijms22126600 · 2021 · External reference
Assessing Glycosphingolipid Profiles in Human Health and Disease Using Non-Imaging MALDI Mass Spectrometry
10.3390/app13179922 · 2023 · External reference
10.1002/1873-3468.13980
10.1002/1873-3468.13980 · External reference
10.1023/a:1011062223612
10.1023/a:1011062223612 · External reference
GD3-and O-acetylated GD3-gangliosides in the GM2 synthase-deficient mouse brain and their immunohistochemical localization. Proceedings of the Japan Academy
2006 · External reference
Unresolved reference
External reference
10.1021/acs.analchem.2c03939
10.1021/acs.analchem.2c03939 · External reference
Advances in mass spectrometry of lipids for the investigation of Niemann-pick type C disease
10.1186/s12944-025-02675-7 · 2025 · External reference
10.1021/cr3004295
10.1021/cr3004295 · External reference
10.1007/s00216-019-01989-7
10.1007/s00216-019-01989-7 · External reference
Trapped Ion Mobility Spectrometry and Parallel Accumulation– Serial Fragmentation in Proteomics
10.1016/j.mcpro.2021.100138 · 2021 · External reference
MALDI TIMS IMS Reveals Ganglioside Molecular Diversity within Murine S. aureus Kidney Tissue Abscesses
10.1021/jasms.4c00089 · 2024 · External reference
Gas-phase separation using a trapped ion mobility spectrometer
2011 · External reference
AP-MALDI Mass Spectrometry Imaging of Gangliosides Using 2,6-Dihydroxyacetophenone
10.1007/s13361-018-1928-8 · 2018 · External reference
10.1002/jms.1367
10.1002/jms.1367 · External reference
Deep MALDI-MS spatial omics guided by quantum cascade laser mid-infrared imaging microscopy
10.1038/s41467-025-59839-3 · 2025 · External reference
10.1002/rcm.10006
10.1002/rcm.10006 · External reference
10.15252/emmm.201506078
10.15252/emmm.201506078 · External reference
10.1093/nar/gkm324
10.1093/nar/gkm324 · External reference
Niemann-Pick disease type C
10.1186/1750-1172-5-16 · 2010 · External reference
10.3389/fnins.2020.572965
10.3389/fnins.2020.572965 · External reference
10.1096/fj.05-4911fje
10.1096/fj.05-4911fje · External reference
10.3390/ijms222111358
10.3390/ijms222111358 · External reference
Cell-Type- and Brain-Region-Resolved Mouse Brain Lipidome
10.1016/j.celrep.2020.108132 · 2020 · External reference
10.1002/1873-3468.13114
10.1002/1873-3468.13114 · External reference
10.1194/jlr.d800038-jlr200
10.1194/jlr.d800038-jlr200 · External reference
Analysis and Comparison of Mouse and Human Brain Gangliosides via Two-Stage Matching of MS/MS Spectra
10.1021/acsomega.1c07070 · 2022 · External reference
10.1016/j.ajpath.2011.04.017
10.1016/j.ajpath.2011.04.017 · External reference
10.3390/ijms23116312
10.3390/ijms23116312 · External reference
10.1038/sj.ejhg.5200272
10.1038/sj.ejhg.5200272 · External reference
Sensitive and Structure-Informative N-Glycosylation Analysis by MALDI-MS; Ionization
2017 · External reference
GD3- and O-acetylated GD3-gangliosides in the GM2 synthase-deficient mouse brain and their immunohistochemical localization
10.2183/pjab.82.189 · 2006 · External reference
Determination of Sialic Acid Isomers from Released N-Glycans Using Ion Mobility Spectrometry
10.1021/acs.analchem.2c00783 · 2022 · External reference
10.1002/1873-3468.13114
10.1002/1873-3468.13114 · ExternalCitation · doi-reference
10.1002/1873-3468.13980
10.1002/1873-3468.13980 · ExternalCitation · doi-reference
10.1002/jms.1367
10.1002/jms.1367 · ExternalCitation · doi-reference
10.1002/rcm.10006
10.1002/rcm.10006 · ExternalCitation · doi-reference
10.1007/s00216-019-01989-7
10.1007/s00216-019-01989-7 · ExternalCitation · doi-reference
AP-MALDI Mass Spectrometry Imaging of Gangliosides Using 2,6-Dihydroxyacetophenone
10.1007/s13361-018-1928-8 · ExternalCitation · doi-reference
10.1016/j.ajpath.2011.04.017
10.1016/j.ajpath.2011.04.017 · ExternalCitation · doi-reference
Cell-Type- and Brain-Region-Resolved Mouse Brain Lipidome
10.1016/j.celrep.2020.108132 · ExternalCitation · doi-reference
10.1016/j.febslet.2010.04.047
10.1016/j.febslet.2010.04.047 · ExternalCitation · doi-reference
Trapped Ion Mobility Spectrometry and Parallel Accumulation– Serial Fragmentation in Proteomics
10.1016/j.mcpro.2021.100138 · ExternalCitation · doi-reference
Determination of Sialic Acid Isomers from Released N-Glycans Using Ion Mobility Spectrometry
10.1021/acs.analchem.2c00783 · ExternalCitation · doi-reference
10.1021/acs.analchem.2c03939
10.1021/acs.analchem.2c03939 · ExternalCitation · doi-reference
Analysis and Comparison of Mouse and Human Brain Gangliosides via Two-Stage Matching of MS/MS Spectra
10.1021/acsomega.1c07070 · ExternalCitation · doi-reference
10.1021/cr3004295
10.1021/cr3004295 · ExternalCitation · doi-reference
MALDI TIMS IMS Reveals Ganglioside Molecular Diversity within Murine S. aureus Kidney Tissue Abscesses
10.1021/jasms.4c00089 · ExternalCitation · doi-reference
10.1023/a:1011062223612
10.1023/a:1011062223612 · ExternalCitation · doi-reference
Deep MALDI-MS spatial omics guided by quantum cascade laser mid-infrared imaging microscopy
10.1038/s41467-025-59839-3 · ExternalCitation · doi-reference
10.1038/sj.ejhg.5200272
10.1038/sj.ejhg.5200272 · ExternalCitation · doi-reference
Neurons in Niemann-Pick Disease Type C Accumulate Gangliosides as Well as Unesterified Cholesterol and Undergo Dendritic and Axonal Alterations
10.1093/jnen/60.1.49 · ExternalCitation · doi-reference
10.1093/nar/gkm324
10.1093/nar/gkm324 · ExternalCitation · doi-reference
10.1096/fj.05-4911fje
10.1096/fj.05-4911fje · ExternalCitation · doi-reference
Niemann-Pick disease type C
10.1186/1750-1172-5-16 · ExternalCitation · doi-reference
Advances in mass spectrometry of lipids for the investigation of Niemann-pick type C disease
10.1186/s12944-025-02675-7 · ExternalCitation · doi-reference
Endothelial and neuronal engagement by AAV-BR1 gene therapy alleviates neurological symptoms and lipid deposition in a mouse model of Niemann-Pick type C2
10.1186/s12987-025-00621-4 · ExternalCitation · doi-reference
10.1194/jlr.d086090
10.1194/jlr.d086090 · ExternalCitation · doi-reference
10.1194/jlr.d800038-jlr200
10.1194/jlr.d800038-jlr200 · ExternalCitation · doi-reference
10.15252/emmm.201506078
10.15252/emmm.201506078 · ExternalCitation · doi-reference
GD3- and O-acetylated GD3-gangliosides in the GM2 synthase-deficient mouse brain and their immunohistochemical localization
10.2183/pjab.82.189 · ExternalCitation · doi-reference
10.3389/fnins.2020.572965
10.3389/fnins.2020.572965 · ExternalCitation · doi-reference
Assessing Glycosphingolipid Profiles in Human Health and Disease Using Non-Imaging MALDI Mass Spectrometry
10.3390/app13179922 · ExternalCitation · doi-reference
Neurodegeneration in Niemann–Pick Type C Disease: An Updated Review on Pharmacological and Non-Pharmacological Approaches to Counteract Brain and Cognitive Impairment
10.3390/ijms22126600 · ExternalCitation · doi-reference
10.3390/ijms222111358
10.3390/ijms222111358 · ExternalCitation · doi-reference
10.3390/ijms23116312
10.3390/ijms23116312 · ExternalCitation · doi-reference