Dilated Endocardial Fibroelastosis: Unusual Late Finding with Congenital Hydrops

The case of a baby born with severe nonimmune hydrops fetalis in whom endocardial fibroelastosis was a late finding is reported. Left ventricular dimensions and systolic function were normal at presentation. After recovery from the hydrops, at 2 months of age, a dilated, poorly contracting left ventricle was documented and eventually led to the infant's death.