Abstract
The presentation of a renal mass presumes a malignancy unless proven otherwise by histologic evaluation. We present a case of 40-year-old man with advance uremia necessitating renal replacement. Radiologic images showed a right renal mass and the patient underwent a nephrectomy. The pathologic diagnosis was a benign renal neoplasm, oncocytoma. This neoplasm is not a cause of renal failure but may be associated with other malignant lesions. Focal segmental glomerulosclerosis was the reason for renal failure. Lesion was discovered incidentally during the workup of chronic kidney disease. Histopathology delineated two separate pathologies designing the management plan. After few months of hemodialysis patient could receive renal transplant, a therapy of choice as oncocytoma is a benign condition which doesn’t preclude transplantation.