Abstract
Coronary artery aneurysm (CAA) is defined as abnormal dilatation of the coronary artery more than 1.5 times the diameter of the normal reference segment of that coronary artery. The incidence is about 1.5-5% and more common in the right coronary artery. The coronary artery aneurysm is classified into saccular or fusiform types, and the CAA is identified as giant if the diameter is more than 20 mm. The etiology of CAA is variable and can be due to genetic causes, inflammatory or autoimmune diseases (vasculitis such as Kawasaki disease, Takayasu arteritis, systemic lupus erythematosus and Marfan syndrome), atherosclerotic cause, infectious causes, cocaine use; and post coronary artery stenting. We present a case of coronary artery aneurysm in a patient who is a known case of lupus nephritis.