Abstract
Low-grade fibromyxoid sarcoma (LGFS) is a rare, indolent spindle cell sarcoma with a risk of recurrence and metastasis. We report the case of a 34-year-old man with a tumor in his thumb that had recurred after excision eight years ago, with slow and progressive growth. The pathological examination was suggestive of SFBG, and we proceeded with the disarticulation of the phalanx. The patient remains in follow-up, with no evidence of metastases. Although rare, it is essential to recognize the diagnosis of an LGFS with its potential risk of recurrences and metastases, especially as a differential diagnosis of acral soft tissue tumors.